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Keratoderma

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Classification

The keratodermas are classified into the following subgroups:

Congenital

  • Simple keratodermas
    • Diffuse palmoplantar keratodermas
      • Diffuse epidermolytic palmoplantar keratoderma
      • Diffuse nonepidermolytic palmoplantar keratoderma
      • mal de Meleda
    • Focal palmoplantar keratoderma
      • Striate palmoplantar keratoderma
    • Punctate palmoplantar keratoderma
      • Keratosis punctata palmaris et plantaris
      • Spiny keratoderma
      • Focal acral hyperkeratosis
  • Complex keratodermas
    • Diffuse palmoplantar keratoderma
    • Focal palmoplantar keratoderma
      • Papillon–Lefèvre syndrome
      • Pachyonychia congenita type I
      • Pachyonychia congenita type II
      • Focal palmoplantar keratoderma with oral mucosal hyperkeratosis
      • Camisa disease
    • Ectodermal dysplasias
      • Clouston's hidrotic ectodermal dysplasia
      • Acrokeratotic poikiloderma
      • Dermatopathic pigmentosa reticularis
    • Syndromic keratodermas
      • Vohwinkel syndrome
      • Palmoplantar keratoderma associated with esophageal cancer
      • Palmoplantar keratoderma and spastic paraplegia
      • Naxos disease
      • Striate palmoplantar keratoderma, woolly hair, and left ventricular dilated cardiomyopathy
      • Keratitis-ichthyosis-deafness syndrome
      • Corneodermatosseous syndrome
      • Huriez syndrome
      • Oculocutaneous tyrosinemia
      • Cardiofaciocutaneous syndrome
      • Schöpf–Schulz–Passarge syndrome

Acquired

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